What Is Prion Protein? | What Is Prion Disease In Humans?
What Is Prion Protein?
Prion protein is a type of protein that can trigger regular proteins in the brain to fold abnormally. The prion protein is then able to induce the same abnormal folding in the regular versions of the same protein, increasing its numbers.
A commenter on Quora, in response to the question, “What is prion protein?” explained it better than I could:
“…The issue is that these prions lead to the formation of plaques within the cell and on the cell surface leading to debilitating symptoms, an example is ‘mad cow’ disease. For humans, once you exhibit the symptoms, the infection has already spread to your brain and it is too late”.
What is Prion Disease?
Prion diseases are caused by normal proteins, which live on the surface of many cells, becoming mutated (folded), and they clump together in the brain, causing damage to the brain. This abnormal build-up of protein in the brain leads to impaired memory and other cognitive problems (including dementia), changes in personality, tics and seizures, hallucinations, and impaired movement.
These disorders caused by prion proteins are basically the result of a constant torrent of mutated protein building up, and this unrelenting cascade of mutant proteins is virtually unstoppable, certainly irreversible, and ultimately (and often very swiftly) fatal.
Prion diseases are collectively known as transmissible spongiform encephalopathies (TSE)
What is Prion Disease In Humans? | Types of Prion Diseases
Prion diseases occur in humans, as well as animals. An example of prion disease in animals would be mad cow disease, or variant Creutzfeldt-Jakob disease (vCJD), which humans can contract.
Mad cow disease is also known as bovine spongiform encephalopathy. So what is prion disease in humans, aside from mad cow disease? Or is it all the same?
Well, it is essentially the same. All of the variants begin with proteins that fold, irregularly.
There are five known types of prion diseases in humans which are currently known, but newer types of prion disease are being recognized, as well.
Creutzfeldt-Jakob disease (CJD), variant Creutzfeldt-Jakob disease (vCJD), Gerstmann-Straussler-Scheinker syndrome (GSS), kuru, and fatal familial insomnia (FFI) are the five we have known about for awhile.
The type that we are probably the most familiar with is vCJD, also known as mad cow disease. In the case of vCJD, the prion is harbored in a living cow (and occasionally a sheep, deer or elk), before it ever becomes food, or a Fonzie jacket.
How Do You Get Prion Disease? Are Prion Proteins Contagious? How Are Prions Transmitted?
Are prion proteins contagious?
In 2004, a report revealed that vCJD can be transmitted by blood transfusions. They are known to be transmitted via improperly sterilized surgical tools, though this is said to be rare. They are more commonly transmitted through eating beef (and some wild animals, but not often).
Copper exposure is always something to avoid, but on the molecular level, copper ions have now been shown to be the cause of prions misfolding, before spreading that mutation to other prions.
How Else Do You Get Prion Disease?
There are two words that you hear about 5,000 times a day, these days, which I have resolved to never dignify by giving “utterance” to on this blog. I don’t even like saying them out loud when I am by myself (yes, I talk to myself).
You know what I am talking about, and the thing behind one of those words is going to kill many, many people. Why?
Because it contains prion proteins!
Can Prions Be Destroyed?
Is it possible to destroy prion proteins? No.
Prions are forever. You’re buying the farm with prion proteins. And I have never said that about anything.
I have come to believe that everything is curable. Unfortunately, I have not been able to find anywhere, anything stating that there is any way to cure prion diseases. They are resistant to heat, radiation and formaldehyde. The only way to destroy them in cattle is incineration.
Prion Disease Symptoms
You can have prion disease for years, before you notice any symptoms. Once symptoms do show up, they then advance very quickly. You will notice decline in brain function, like memory loss, behavioural and personality changes, anxiety and/or depression, slurred speech and possible seizures, as well as vision problems and shakes, and loss of motor skill function and muscle control.
What Are the Chances of Getting Prion Disease?
The chances of getting prion disease are slim, unless you eat a lot of infected meat (particularly beef). The chances of
getting prion disease are much greater if you eat the brain of an infected cow, or its spinal column. Or…
Contracting prion disease is nearly inevitable if you are administered certain injections being pushed these days. Prion disease will be among the many other complications you will experience, at some point, if you receive these shots. Some of these could likely be reversible, but as we have established, you will not get rid of prions, they are like tiny Terminators in your brain cells and nervous system.
Prion Disease Prevention
Prion disease prevention is pretty simple. Know where the meat you are eating comes from (or just don’t eat it), and don’t let anyone stick anything in you that is deadly. And if you don’t believe that these things are deadly, then you had better start believing it. There is no longer any reason anyone should be ignorant to this fact. All you have to do is be willing to believe it, and have the courage to look. There is solid evidence everywhere.
And there is NO actual evidence to the contrary!
Mad Cowboy Book by Howard F. Lyman
Mad Cowboy is an impassioned account of the highly dangerous practices of the cattle and dairy industries. Howard Lyman’s testimony on The Oprah Winfrey Show revealed the deadly impact of the livestock industry on our well-being… it sent shock waves through a concerned and vulnerable public. A fourth-generation Montana rancher, Lyman investigated the use of chemicals in agriculture after developing a spinal tumor that nearly paralyzed him.
Now a vegetarian, he blasts through the propaganda of beef and dairy interests—and the government agencies that protect them—to expose an animal-based diet as the primary cause of cancer, heart disease, and obesity in this country. He warns that the livestock industry is repeating the mistakes that led to Mad Cow disease in England while simultaneously causing serious damage to the environment. Persuasive, straightforward, and full of the down-home good humor and optimism of a son of the soil, Mad Cowboy is both an inspirational story of personal transformation and a convincing call to action for a plant-based diet—for the good of the planet and the health of us all.
I hope this has adequately explained some things you didn’t know before, like what prions are, what prion disease is in humans and animals, how do you get prion disease, and what are the chances of getting prion disease and how to prevent getting it.
The aim has been to show the different types of prion diseases and their symptoms, and that prion disease is no joke. Prions cannot be destroyed (yet), and are ultimately deadly.
And if I haven’t made it crystal clear yet, I need to emphasize that prions are now being willfully and tyrannically injected into people, including young children, and this is grossly deplorable, and unacceptable.
If you have explored the information linked to in this article, you will now understand the depth and breadth of this evil, and if you are like me, it will make you seriously reconsider some things, including what you eat and don’t eat, in the future.
Thanks for taking the time.